Distraction Osteogenesis in Silver Russell Syndrome to Expand the Mandible

Reha S. KISNISCI, Stephen D. FOWEL, Bruce N. EPKER

Distraction osteogenesis is a method commonly used to active bone regeneration in nonunions and osseous defects and for lengthening procedures of tubular bones. This technique involves the sectioning of a bone and the subsequent deliberate, controlled movement of the opposing sectioned edges to lengthen, widen, or reposition a bone, or all three. In this report, a patient with Silver Russell syndrome and severe mandibular hypoplasia was treated by means of distraction osteogenesis of the midsymphysis to widen the mandible in concert with sagittal-ramus osteotomies to lengthen the mandible. This treatment created significantly increased arch length in the mandible, which was necessary to facilitate the patientís orthodontic treatment. We believe this is the first reported case of distraction osteogenesis to widen the mandible with the use of a tooth-borne appliance.

Keywords: Distraction osteogenesis. Silver Russell Syndrome. Mandibular expansion. Mandibular hypoplasia. Orthognathic surgery. Sagital-ramus osteotomy.

Monday, April 29, 2024 03:27