Orthodontic Treatment of a Pacient with Incontinentia Pigmenti: Case Report

Maria Helena Ferreira VASCONCELOS, Renato Rodrigues de ALMEIDA, Guilherme JANSON

Incontinentia pigmenti is an uncommmon syndromic disease, affecting the skin and correlated organs, probably of genetic origin with a x-linked dominant mode of inheritance. The most striking features of the syndrome are vesiculo-bullous skin lesions and patches of melanin pigmentation. Other characteristics include ocular anomalies, disorders of the central nervous system, and dental anomalies, as partial anodontia and the presence of some peg-shaped teeth and/or hypoplasics. Late eruption of teeth is also observed in some cases. This article will discuss the aspects of this syndrome, presenting a case report of a pacient under orthodontic treatment.

Keywords: Incontinentia Pigmenti. Partial Anodontia. BlochSulzberger Syndrome.

Monday, April 29, 2024 05:03